Bladder Exstrophy and Epispadias: A Compendium

This book brings together contemporary experts in bladder exstrophy-epispadias from around the world to present evidence-based recommendations for managing this anomaly from prenatal diagnosis, postnatal management, surgical reconstruction, long-term management, sexual and fertility implications, and psychosocial impacts on the patient, family and immediate community ecosystem. Bladder exstrophy and epispadias is relatively rare in its incidence, but remains, perhaps, the most complex congenital anomaly faced by pediatric urologists. When presented with an infant with this anomaly, there remains great controversy in every aspect of management of this disorder—from what causes it, to when it should be repaired, to how it should be repaired, and what long-term management should entail. Pediatric urologists are only now beginning to seriously explore new strategies in dealing with bladder exstrophy, and long-term studies are being initiated and completed presenting a clearer picture on how this anomaly—with serious long-term consequences—should be managed. Moreover, bladder exstrophy is a global problem and its incidence is greater in the developing world.

Bladder Exstrophy and Epispadias: A Compendium begins by covering diagnosis and imaging, followed by surgical considerations and expected outcomes of repair. From here, various surgical repair methods, like complete primary repair, modern staged repair, Kelly repair, and various alternative approaches are covered in detail. A video library offering step by step depictions of each of the surgical approaches for bladder exstrophy, epispadias and cloacal exstrophy repairs offers the reader a unique, invaluable resource. This book is unique in including a global perspective on how this condition should be addressed in the face of disparities in access to care—especially in the Global South. Finally, a discussion of long-term results and the gynecological implications of exstrophy leads into a view of the patient and family perspective.

This is an ideal guide for urologists, pediatric urologists, surgeons, and students to be able to successfully diagnose, treat, and manage bladder exstrophy and epispadias.

Aseem Ravindra Shukla, MD, MHCI, Endowed Chair and Director of Minimally Invasive Surgery, Children’s Hospital of Philadelphia, Professor of Surgery (Urology) Perelman School of Medicine, University of Pennsylvania

Rakesh S. Joshi, M. Ch., Head of Department, Paediatric Surgery, Superintendent/CEO, Civil Hospital, Ahmedabad, India

Joao Luiz Pippi Salle, MD, PhD, FAAP, FRCSC
Professor of Urology, Division of Urology, Toronto Hospital for Sick Kids
Inaugural Chair Women's Auxiliary Chair in Urology
Toronto, Canada

Paul A. Merguerian MD MS

Professof of Urology

University of Washington

Seattle Children’s Hospital

Seattle, Washington, USA

Pramod Reddy, MD, The Curtis Sheldon and Jeffrey Wacksman Chair of Pediatric Urology, Janszen Endowed Scholar in Urology, Director, Division of Pediatric Urology, Cincinnati Children’s, Professor of Urology – Univ of Cincinnati College of Medicine, Cincinnati, Ohio. 

Jaishri Ramji, M.Ch
Professor, Department of Pediatric Surgery, B.J.Medical College and Civil Hospital, Ahmedabad.

Dana A. Weiss, MD
Howard M. Snyder III Endowed Chair in Pediatric Urology, Associate Professor of Urology (in Surgery), Children's Hospital of Philadelphia, Perelman School of Medicine at the University of Pennsylvania